What neurological symptom can present in Sturge-Weber syndrome?

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Sturge-Weber syndrome is a neurocutaneous disorder characterized by the presence of a facial capillary malformation (port-wine stain) and leptomeningeal angiomatosis, which can lead to a range of neurological symptoms due to associated cortical dysplasia and seizures.

Dystonia can often be seen in patients with Sturge-Weber syndrome due to the brain malformations and the effects of seizures on motor control. Dystonia involves sustained muscle contractions, abnormal postures, or twisting movements, which can be attributed to changes in the basal ganglia or motor cortex function impacted by the underlying vascular lesions.

While hypotonia and spasticity can also present in patients with various neurological disorders, they are not as specifically associated with Sturge-Weber syndrome as dystonia. Hypotonia involves decreased muscle tone and spasticity involves increased muscle tone and reflexes, which are commonly seen in other conditions but may not be the most prominent in this particular syndrome.

Given that dystonia demonstrates a clear association with the neurological aspects of Sturge-Weber syndrome, it is recognized as a significant symptom. Thus, focusing on dystonia provides a targeted understanding of the neurologic manifestations related to this syndrome.

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